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Dosing DOJOLVI (triheptanoin).

UNDERSTANDING DOJOLVI DOSING

Dosing for DOJOLVI is individualized based on patient tolerability, medical needs, and other dietary requirements.1,2

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Understanding DOJOLVI Dosing Guide

HOW THE DOJOLVI DOSE IS CALCULATED2

The recommended target daily dosage of DOJOLVI (triheptanoin) is up to 35% of the patient’s total prescribed daily caloric intake (DCI), divided into four or more doses and mixed thoroughly into semisolid food/liquid or medical food/formula at mealtimes or with snacks.*

Assess the metabolic requirements of the patient by determining their DCI prior to calculating the dose of DOJOLVI.

To find the DOJOLVI dose for your patient:

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1. MULTIPLY

MULTIPLY the total DCI (in kcal) by the target percentage of the DCI that will be provided by DOJOLVI

Total DCI (kcal) x target % of DCI formula

2. DIVIDE

DIVIDE by 8.3 kcal/mL, the caloric value of DOJOLVI

DIVIDE by 8.3 kcal/mL, the caloric value of DOJOLVI

3. ROUND

ROUND the calculated total daily dosage of DOJOLVI (in mL) to the nearest whole number

Image of total daily dosage (in mL) to be filled in

4. DIVIDE

DIVIDE the total daily dosage into at least 4 approximately equal doses to be given at each interval mixed thoroughly with a meal or snack

Image of mL per dose to be filled in

In order to reach a target daily dosage, patients may require an increase in their total fat intake. All patients treated with DOJOLVI should be under the care of a clinical specialist knowledgeable in appropriate disease-related dietary management based upon current nutritional recommendations.

The neonatal population may require higher fat intake and therefore an increased amount of DOJOLVI. Current nutritional recommendations should be considered when dosing the neonatal population.

Initiating and titrating DOJOLVI2

For patients not currently taking a medium-chain triglyceride (MCT) product:

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Initiate DOJOLVI (triheptanoin) at a total daily dosage of approximately 10% DCI, divided into at least 4 times per day. Increase to the recommended total daily dosage by approximately 5% DCI every 2 to 3 days until the target dosage of up to 35% DCI is achieved.


For patients switching from another MCT product:

medium-chain triglyceride icon

Discontinue use of MCT products before starting DOJOLVI.

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Initiate DOJOLVI at the last tolerated daily dosage of MCT divided into at least 4 times per day. Increase the total daily dosage by approximately 5% DCI every 2 to 3 days until the target dosage of up to 35% DCI is achieved.

Tolerability:

Consider more frequent, smaller doses if a patient has difficulty tolerating 1/4 of the total daily dosage at one time based on gastrointestinal adverse reactions.

Monitor the patient’s total caloric intake during dosage titration, especially in a patient with gastrointestinal adverse reactions, and adjust all components of the diet as needed.

If a patient experiences gastrointestinal adverse reaction(s), consider dosage reduction until the gastrointestinal symptoms resolve.

If a patient is unable to achieve the target daily dosage of up to 35% DCI during dosage titration, maintain the patient at the maximum tolerated dosage.

Do not administer DOJOLVI alone to avoid gastrointestinal upset and feeding tube degradation.

USING THE DOJOLVI CALCULATOR

Designed to help determine the DOJOLVI daily dosing schedule for your patients, the DOJOLVI Dosing Calculator can be used to:

  • Determine dosing for all patients ready to start DOJOLVI. This includes patients:
    • Not currently taking another medium-chain triglyceride (MCT) product
      OR
    • Switching from another MCT product
  • Output reports for your records
  • Support your patients with a customized dosing schedule

Calculate DOJOLVI Now

DOJOLVI® (triheptanoin) Dosing Calculator Screen

Administering DOJOLVI2

daily icon

Administer DOJOLVI (triheptanoin) at least 4 times per day orally or via oral or enteral feeding tubes manufactured of silicone or polyurethane


syringe icon

Use an oral syringe or measuring cup made of compatible materials to withdraw the prescribed volume of DOJOLVI from the bottle

  • Compatible materials include stainless steel, glass, high-density polyethylene (HDPE), polypropylene, low-density polyethylene (LDPE), polyurethane, and silicone
  • Do not prepare or administer DOJOLVI using containers, oral syringes, or measuring cups made of polystyrene or polyvinyl chloride (PVC) plastics
  • Regularly monitor the containers, dosing components, or utensils that are in contact with DOJOLVI to ensure proper functioning and integrity

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Add the prescribed amount of DOJOLVI to a clean bowl, cup, or container made of compatible materials, which contains an appropriate amount of semisolid food/liquid or medical food/formula, and mix or emulsify thoroughly


drink icon

To minimize gastrointestinal upset when taken orally, always mix DOJOLVI thoroughly with semisolid food or liquid such as:

  • Plain or artificially sweetened fat-free yogurt
  • Fat-free milk, formula, or cottage cheese
  • Whole-grain hot cereal
  • Fat-free, low-carbohydrate pudding, smoothies, applesauce, or baby food

The unused DOJOLVI mixture may be stored for up to 24 hours in the refrigerator.

If not used within 24 hours, dispose of the DOJOLVI mixture in the trash. Do not pour down the sink. Do not save for later.

If a dose is missed, take the next dose as soon as possible, with subsequent doses taken at 3- to 4-hour intervals. Skip the missed dose if it will not be possible to take all 4 doses in a day.

To help avoid gastrointestinal upset and feeding tube degradation, mix or emulsify DOJOLVI thoroughly into the medical food or formula. Do not administer DOJOLVI alone.

DOJOLVI is administered as an oral or enteral bolus medication. Do not add DOJOLVI to the feeding bag, as the feeding equipment may degrade over time. Feeding tube performance and functionality can degrade over time depending on usage and environmental conditions. In clinical trials, feeding tube dysfunction was reported in patients receiving triheptanoin.

Avoid administration of DOJOLVI in patients with pancreatic insufficiency.

For complete information on the preparation and administration of DOJOLVI, please refer to Section 2.4 of the full Prescribing Information.

PREPARING DOJOLVI

A video guide for your patients to demonstrate how to use the dosing components to prepare a DOJOLVI dose

Choose video:

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Inserting the press-in bottle adapter

Video 1 – Explore the depths of our planet’s oceans. Experience the stories that connect their world to ours. Lorem ipsum dolor sit amet, consectetur adipiscing elit, sed do eiusmod tempor incididunt ut labore et dolore magna aliqua. Ut enim ad minim veniam, quis nostrud exercitation ullamco laboris nisi ut aliquip ex ea commodo consequat. Duis aute irure dolor in reprehenderit in voluptate velit esse cillum dolore eu fugiat nulla pariatur. Excepteur sint occaecat cupidatat non proident, sunt in culpa qui officia deserunt mollit anim id est laborum.

MIXING DOJOLVI

A video demonstration for your patients on how to properly mix DOJOLVI into semi-solid foods or liquids when preparing to take the medication orally

Do not administer DOJOLVI alone to avoid gastrointestinal upset. If the DOJOLVI mixture is not used within 24 hours, throw away (dispose of) in the trash. Do not pour down the sink. Do not save for later.

For complete information on the preparation and administration of DOJOLVI orally or enterally via a silicone or polyurethane feeding tube, please refer to Section 2.4 of the full Prescribing Information.

Inserting the press-in bottle adapter

Video 1 – Explore the depths of our planet’s oceans. Experience the stories that connect their world to ours. Lorem ipsum dolor sit amet, consectetur adipiscing elit, sed do eiusmod tempor incididunt ut labore et dolore magna aliqua. Ut enim ad minim veniam, quis nostrud exercitation ullamco laboris nisi ut aliquip ex ea commodo consequat. Duis aute irure dolor in reprehenderit in voluptate velit esse cillum dolore eu fugiat nulla pariatur. Excepteur sint occaecat cupidatat non proident, sunt in culpa qui officia deserunt mollit anim id est laborum.

Storing DOJOLVI2

DOJOLVI is a clear, colorless to light yellow liquid supplied in a 500 mL bottle containing 100% w/w of triheptanoin.

temperature icon

Store DOJOLVI upright at room temperature between 68° and 77°F (20° and 25°C)

do not freeze icon

Do not freeze DOJOLVI

expire icon

Opened bottles of DOJOLVI can be used for up to 9 months after opening, but not beyond the expiration date on the bottle

caution icon

Do not store DOJOLVI in containers made of polystyrene or polyvinyl chloride (PVC)

DOJOLVI® (triheptanoin) product image

dosing guide

Provide your patients and their caregivers with a step-by-step guide for storing, administering, and keeping track of DOJOLVI doses.

DOJOLVI® (triheptanoin) Dosing Guide

Download the Guide

References:

  1. Data on file. Ultragenyx CL201 CSR. Ultragenyx Pharmaceutical Inc.; 2017.
  2. DOJOLVI (triheptanoin) US Prescribing Information; October 2023.

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FOR US HEALTHCARE PROFESSIONALS

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Ultragenyx will not sell, rent, or otherwise distribute your name and any personally identifiable information outside of Ultragenyx and its agents. Ultragenyx will only use your information in accordance with its Privacy Policy.

INDICATION

DOJOLVI is a medium-chain triglyceride indicated as a source of calories and fatty acids for the treatment of adult and pediatric patients with molecularly confirmed long-chain fatty acid oxidation disorders (LC-FAOD).

IMPORTANT SAFETY INFORMATION

WARNINGS AND PRECAUTIONS

Feeding Tube Dysfunction

  • Feeding tube performance and functionality can degrade over time depending on usage and environmental conditions. In clinical trials, feeding tube dysfunction was reported in patients receiving triheptanoin. The contribution of DOJOLVI cannot be ruled out. Do not administer DOJOLVI in feeding tubes manufactured of polyvinyl chloride (PVC). Regularly monitor the feeding tube to ensure proper functioning and integrity.

Intestinal Malabsorption in Patients with Pancreatic Insufficiency

  • Pancreatic enzymes hydrolyze triheptanoin and release heptanoate as medium-chain fatty acids in the small intestine. Low or absent pancreatic enzymes may result in reduced absorption of heptanoate subsequently leading to insufficient supplementation of medium-chain fatty acids. Avoid administration of DOJOLVI in patients with pancreatic insufficiency.

ADVERSE REACTIONS

Gastrointestinal (GI)

  • The most common GI-related adverse reactions reported in the pooled safety population of Studies 1 and 2 were abdominal pain (abdominal discomfort, abdominal distension, abdominal pain, abdominal pain upper, GI pain) [60%], diarrhea [44%], vomiting [44%], and nausea [14%].

DRUG INTERACTIONS

Pancreatic Lipase Inhibitors

  • Co-administration of triheptanoin with a pancreatic lipase inhibitor (e.g., orlistat) may reduce exposure to the triheptanoin metabolite, heptanoate, and reduce the clinical effect of triheptanoin. Avoid co-administration of DOJOLVI with pancreatic lipase inhibitors.

USE IN SPECIFIC POPULATIONS

Pregnancy and Lactation

  • There are no available data on triheptanoin use in pregnant women to evaluate for a drug-associated risk of major birth defects, miscarriage, or adverse maternal or fetal outcomes. There is a pregnancy safety study for DOJOLVI. If a patient becomes pregnant while receiving DOJOLVI, healthcare providers should report DOJOLVI exposure by calling Ultragenyx Pharmaceutical Inc. at 1-888-756-8657.
  • There are no data on the presence of triheptanoin or its metabolites in human or animal milk, the effects on the breastfed infant, or the effects on milk production. The developmental and health benefits of breastfeeding should be considered along with the clinical need for DOJOLVI and any potential adverse effect on the breastfed infant from DOJOLVI or from the underlying maternal condition.

PATIENT COUNSELING INFORMATION

  • Instruct the patient or caregiver to read the FDA-approved patient labeling, which includes information on the appropriate oral or feeding tube preparation, administration, and storage.

You may report side effects to Ultragenyx Pharmaceutical Inc. at 1-888-756-8657 or FDA at 1-800-FDA-1088 or www.fda.gov/medwatch.


Please see full Prescribing Information for a complete discussion of the risks associated with DOJOLVI.

INDICATION

DOJOLVI is a medium-chain triglyceride indicated as a source of calories and fatty acids for the treatment of adult and pediatric patients with molecularly confirmed long-chain fatty acid oxidation disorders (LC-FAOD).

IMPORTANT SAFETY INFORMATION

WARNINGS AND PRECAUTIONS

Feeding Tube Dysfunction

  • Feeding tube performance and functionality can degrade over time depending on usage and environmental conditions. In clinical trials, feeding tube dysfunction was reported in patients receiving triheptanoin. The contribution of DOJOLVI cannot be ruled out. Do not administer DOJOLVI in feeding tubes manufactured of polyvinyl chloride (PVC). Regularly monitor the feeding tube to ensure proper functioning and integrity.

Intestinal Malabsorption in Patients with Pancreatic Insufficiency

  • Pancreatic enzymes hydrolyze triheptanoin and release heptanoate as medium-chain fatty acids in the small intestine. Low or absent pancreatic enzymes may result in reduced absorption of heptanoate subsequently leading to insufficient supplementation of medium-chain fatty acids. Avoid administration of DOJOLVI in patients with pancreatic insufficiency.

ADVERSE REACTIONS

Gastrointestinal (GI)

  • The most common GI-related adverse reactions reported in the pooled safety population of Studies 1 and 2 were abdominal pain (abdominal discomfort, abdominal distension, abdominal pain, abdominal pain upper, GI pain) [60%], diarrhea [44%], vomiting [44%], and nausea [14%].

DRUG INTERACTIONS

Pancreatic Lipase Inhibitors

  • Co-administration of triheptanoin with a pancreatic lipase inhibitor (e.g., orlistat) may reduce exposure to the triheptanoin metabolite, heptanoate, and reduce the clinical effect of triheptanoin. Avoid co-administration of DOJOLVI with pancreatic lipase inhibitors.

USE IN SPECIFIC POPULATIONS

Pregnancy and Lactation

  • There are no available data on triheptanoin use in pregnant women to evaluate for a drug-associated risk of major birth defects, miscarriage, or adverse maternal or fetal outcomes. There is a pregnancy safety study for DOJOLVI. If a patient becomes pregnant while receiving DOJOLVI, healthcare providers should report DOJOLVI exposure by calling Ultragenyx Pharmaceutical Inc. at 1-888-756-8657.
  • There are no data on the presence of triheptanoin or its metabolites in human or animal milk, the effects on the breastfed infant, or the effects on milk production. The developmental and health benefits of breastfeeding should be considered along with the clinical need for DOJOLVI and any potential adverse effect on the breastfed infant from DOJOLVI or from the underlying maternal condition.

PATIENT COUNSELING INFORMATION

  • Instruct the patient or caregiver to read the FDA-approved patient labeling, which includes information on the appropriate oral or feeding tube preparation, administration, and storage.

You may report side effects to Ultragenyx Pharmaceutical Inc. at 1-888-756-8657 or FDA at 1-800-FDA-1088 or www.fda.gov/medwatch.


Please see full Prescribing Information for a complete discussion of the risks associated with DOJOLVI.